{"created":"2024-07-25T01:31:47.194444+00:00","id":2000461,"links":{},"metadata":{"_buckets":{"deposit":"fdf9e1de-e40f-49ce-91c7-26f91509c751"},"_deposit":{"created_by":50,"id":"2000461","owner":"50","owners":[50],"pid":{"revision_id":0,"type":"depid","value":"2000461"},"status":"published"},"_oai":{"id":"oai:kagawa-u.repo.nii.ac.jp:02000461","sets":["2:1720746067615:1721712715562"]},"author_link":["4301","4299","1564","751","4302","4300","2878","4303"],"control_number":"2000461","item_10001_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2013-09-01","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1","bibliographicPageEnd":"38","bibliographicPageStart":"35","bibliographicVolumeNumber":"15","bibliographic_titles":[{"bibliographic_title":"香川産科婦人科雑誌","bibliographic_titleLang":"ja"},{"bibliographic_title":"Kagawa journal of obstetrics and gynecology : official journal of the Kagawa Society of Obstetrics and Gynecology","bibliographic_titleLang":"en"}]}]},"item_10001_description_5":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"血栓性血小板減少性紫斑病(TTP)は、①細血管障害性溶血性貧血、②破壊性血小板減少症、③血小板血栓による臓器障害、④発熱、⑤動揺性精神神経障害、の古典的5徴候(pentad)を特徴とする重篤な疾患である。TTP患者では止血因子von Willebrand因子(VWF)特異的切断酵素であるADAMTS13の活性が先天的または後天的に低下しており、ADAMTS13活性が診断の指標とされるようになった。TTPはまれな疾患ではあるが、早期に診断し適切な治療を開始しなければ死に至ることもあり得る。妊娠・分娩などを契機に発症することもあり、鑑別すべきものとして妊娠性血小板減少症、特発性血小板減少性紫斑病、HELLP症候群などがある。今回我々は分娩を契機に発見された後天性TTPの1例を経験したので報告する。","subitem_description_language":"ja","subitem_description_type":"Abstract"}]},"item_10001_heading_23":{"attribute_name":"見出し","attribute_value_mlt":[{"subitem_heading_banner_headline":"症例報告","subitem_heading_language":"ja"},{"subitem_heading_banner_headline":"[Case 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