| Item type |
学術雑誌論文 / Journal Article(1) |
| 公開日 |
2024-08-01 |
| タイトル |
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|
タイトル |
Perianal alveolar rhabdomyosarcoma with pulmonary lymphangitic sarcomatosis : Report of an autopsy case |
|
言語 |
en |
| 言語 |
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|
言語 |
eng |
| 資源タイプ |
|
|
資源タイプ識別子 |
http://purl.org/coar/resource_type/c_6501 |
|
資源タイプ |
journal article |
| アクセス権 |
|
|
アクセス権 |
open access |
|
アクセス権URI |
http://purl.org/coar/access_right/c_abf2 |
| 著者 |
松本, 晃一
石川, 亮
福家, 典子
横田, 崇之
若林, 誉幸
千葉, 陽一
河内, 真知
岡田, 仁
上野, 正樹
|
| 抄録 |
|
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内容記述タイプ |
Abstract |
|
内容記述 |
Background: Childhood rhabdomyosarcoma (RMS) of perineal or perianal origin (PRMS) is rare, accounting for only 2% of all RMSs. PRMS has been reported to show different characteristics depending on the patient’s age, and patients aged 10 years or older have a poor prognosis. Disseminated intravascular coagulation (DIC) is considered to be an uncommon complication of RMS. However, it could occur occasionally in patients with widespread RMS with bone marrow infiltration. Pulmonary lymphangitic sarcomatosis (PLS) has been reported to be rare, and to our knowledge, only 18 cases (including 4 patients with RMS) have been reported to date. |
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言語 |
en |
| 抄録 |
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内容記述タイプ |
Abstract |
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内容記述 |
Case report: A 15-year-old female patient with suspected RMS was admitted to our hospital. The patient was diagnosed with PRMS following radiological evaluations and effusion cytology, and chemotherapy was initiated on the 6th day of admission. During the course, the patient suffered from severe dyspnea and DIC. Despite treatment, the bleeding tendency did not improve, and hepatic and renal failure progressed. The patient died of progressive respiratory failure on the 13th day of admission. An autopsy, performed 2 h after death, revealed a perianal tumor with pseudoalveolar growth pattern. In the lungs, a relatively large number of small metastatic foci, presumed to be lymphatic spread, were identified. It was diagnosed as PLS due to alveolar RMS. |
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言語 |
en |
| 抄録 |
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内容記述タイプ |
Abstract |
|
内容記述 |
Conclusion: Although PLS is reported to be an unexpected form of metastasis, it might cause severe dyspnea in patients with RMS, as 4 of 18 reported cases of PLS are associated with RMS. |
|
言語 |
en |
| 書誌情報 |
en : Human pathology : Case reports
巻 25,
発行日 2021-09
|
| 出版者 |
|
|
出版者 |
Elsevier |
|
言語 |
en |
| ISSN |
|
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収録物識別子タイプ |
EISSN |
|
収録物識別子 |
2214-3300 |
| 権利 |
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|
言語 |
en |
|
権利情報 |
© 2021 The Author(s). |
| 権利 |
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|
言語 |
en |
|
権利情報Resource |
http://creativecommons.org/licenses/by-nc-nd/4.0/ |
|
権利情報 |
This is an open access article under the CC BY-NC-ND licens. |
| 他の資源との関係 |
|
|
関連タイプ |
isIdenticalTo |
|
|
識別子タイプ |
DOI |
|
|
関連識別子 |
https://doi.org/10.1016/j.ehpc.2021.200544 |
| 著者版フラグ |
|
|
出版タイプ |
VoR |
|
出版タイプResource |
http://purl.org/coar/version/c_970fb48d4fbd8a85 |
| キーワード |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
Perianal alveolar rhabdomyosarcoma |
| キーワード |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
Pulmonary lymphangitic sarcomatosis |
| キーワード |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
Disseminated intravascular coagulation |
| キーワード |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
Effusion cytology |
https://doi.org/10.1016/j.ehpc.2021.200544
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