{"created":"2024-08-22T07:28:59.650765+00:00","id":2000539,"links":{},"metadata":{"_buckets":{"deposit":"0fac8464-2d34-4856-91cb-45c1b7007b3e"},"_deposit":{"created_by":50,"id":"2000539","owner":"50","owners":[50],"pid":{"revision_id":0,"type":"depid","value":"2000539"},"status":"published"},"_oai":{"id":"oai:kagawa-u.repo.nii.ac.jp:02000539","sets":["2:1720746067615:1722583165741"]},"author_link":["4281","4353"],"control_number":"2000539","item_10001_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2023-09-01","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1","bibliographicPageEnd":"27","bibliographicPageStart":"23","bibliographicVolumeNumber":"25","bibliographic_titles":[{"bibliographic_title":"香川産科婦人科雑誌","bibliographic_titleLang":"ja"},{"bibliographic_title":"Kagawa journal of obstetrics and gynecology : official journal of the Kagawa Society of Obstetrics and Gynecology","bibliographic_titleLang":"en"}]}]},"item_10001_description_5":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"妊娠中に母体の一過性大腿骨頭萎縮症による疼痛・歩行障害と分娩後発症の大腿骨頸部骨折をきたし、のちに骨形成不全症を疑った症例を経験した。妊娠前にPreconception care(PCC)を受けていれば骨折を回避できた可能性もあり、改めてPCCの重要性を認識したので報告する。症例は31歳、身長146cm、非妊時体重39.5k、軽度の青色強膜あり。初経13歳、月経整順、1妊0産。既往歴なし、ダイエット歴無し。実母が50歳代から骨粗鬆症にて加療中。自然妊娠成立後、妊娠初期にて当科を受診した。産婦人科の受診は初めてであった。妊娠34週、左股関節痛が出現したが単純X線検査では異常は認められなかった。妊娠38週3日、疼痛のため歩行困難となり選択的帝王切開術を施行した。手術直後の単純X線検査も異常は認められなかった。術後5日目になっても疼痛による歩行困難が改善せず、単純X線検査による再検査で、左大腿骨頸部骨折を認めた。MRIにて大腿骨頸部はT1強調画像で低信号、脂肪抑制のT2強調画像で高信号を示し、一過性大腿骨頭萎縮症と診断した。術後12日目に左大腿骨人工骨頭置換術を施行した。術中所見にて骨の強度の脆弱性が判明した。DEXA法にて骨密度測定を施行し、腰椎YAM59%、右大腿骨頸部YAM52%と骨粗鬆症の所見を認めた。臨床症状と合わせて骨形成不全症が疑われた。テリパラチド投与を開始したが通院中にも胸椎の多発性圧迫骨折を発症した。もし妊娠前にPCCを行い、青色強膜や低身長、母体の若年期骨粗鬆症に注目し、骨系統疾患を疑うことができれば妊娠前に適切な対応ができていた可能性は考えられる。PCC施行時に低身長を認める女性では、青色強膜の現症や骨痛の既往、骨粗鬆症の家族歴等、骨系統疾患の可能性についても注意深く検討する必要があることが示唆された。","subitem_description_language":"ja","subitem_description_type":"Abstract"}]},"item_10001_heading_23":{"attribute_name":"見出し","attribute_value_mlt":[{"subitem_heading_banner_headline":"症例報告","subitem_heading_language":"ja"},{"subitem_heading_banner_headline":"[Case report]","subitem_heading_language":"en"}]},"item_10001_publisher_8":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"香川産科婦人科学会","subitem_publisher_language":"ja"}]},"item_10001_relation_17":{"attribute_name":"関連サイト","attribute_value_mlt":[{"subitem_relation_type":"isPartOf","subitem_relation_type_id":{"subitem_relation_type_id_text":"https://www.med.kagawa-u.ac.jp/~perigyne/ksog/journal/pdf/bukai25.pdf","subitem_relation_type_select":"URI"}}]},"item_10001_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"2185-1409","subitem_source_identifier_type":"EISSN"}]},"item_10001_version_type_20":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_access_right":{"attribute_name":"アクセス権","attribute_value_mlt":[{"subitem_access_right":"open access","subitem_access_right_uri":"http://purl.org/coar/access_right/c_abf2"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorAffiliations":[{"affiliationNameIdentifiers":[{"affiliationNameIdentifier":"","affiliationNameIdentifierScheme":"ISNI","affiliationNameIdentifierURI":"http://www.isni.org/isni/"}],"affiliationNames":[{"affiliationName":"","affiliationNameLang":"ja"}]}],"creatorNames":[{"creatorName":"河西, 邦浩","creatorNameLang":"ja"},{"creatorName":"カワニシ, クニヒロ","creatorNameLang":"ja-Kana"},{"creatorName":"Kawanishi, Kunihiro","creatorNameLang":"en"}],"familyNames":[{"familyName":"河西","familyNameLang":"ja"},{"familyName":"カワニシ","familyNameLang":"ja-Kana"},{"familyName":"Kawanishi","familyNameLang":"en"}],"givenNames":[{"givenName":"邦浩","givenNameLang":"ja"},{"givenName":"クニヒロ","givenNameLang":"ja-Kana"},{"givenName":"Kunihiro","givenNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"4281","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"9000364466748","nameIdentifierScheme":"CiNii ID","nameIdentifierURI":"http://ci.nii.ac.jp/nrid/9000364466748"}]},{"creatorNames":[{"creatorName":"遠藤, 理砂","creatorNameLang":"ja"},{"creatorName":"エンドウ, リサ","creatorNameLang":"ja-Kana"},{"creatorName":"Endo, Risa","creatorNameLang":"en"}],"familyNames":[{"familyName":"遠藤","familyNameLang":"ja"},{"familyName":"エンドウ","familyNameLang":"ja-Kana"},{"familyName":"Endo","familyNameLang":"en"}],"givenNames":[{"givenName":"理砂","givenNameLang":"ja"},{"givenName":"リサ","givenNameLang":"ja-Kana"},{"givenName":"Risa","givenNameLang":"en"}],"nameIdentifiers":[{"nameIdentifier":"4353","nameIdentifierScheme":"WEKO"}]}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"プレコンセプションケア","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"骨形成不全症","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"一過性大腿骨頭萎縮症","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"妊娠","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"骨粗鬆症","subitem_subject_language":"ja","subitem_subject_scheme":"Other"},{"subitem_subject":"Preconception care","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Osteogenesis imperfect","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Transient osteoporosis of the hip","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Pregunancy","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Osteoporosis","subitem_subject_language":"en","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"プレコンセプションケアの重要性を感じた骨形成不全症疑い妊婦の一例","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"プレコンセプションケアの重要性を感じた骨形成不全症疑い妊婦の一例","subitem_title_language":"ja"},{"subitem_title":"Importance of preconception care for a pregnant woman with suspected osteogenesis imperfecta","subitem_title_language":"en"}]},"item_type_id":"10001","owner":"50","path":["1722583165741"],"pubdate":{"attribute_name":"PubDate","attribute_value":"2024-08-22"},"publish_date":"2024-08-22","publish_status":"0","recid":"2000539","relation_version_is_last":true,"title":["プレコンセプションケアの重要性を感じた骨形成不全症疑い妊婦の一例"],"weko_creator_id":"50","weko_shared_id":-1},"updated":"2024-09-25T00:55:31.908911+00:00"}